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Dermatomyositis sine myositis and antisynthetase syndrome.

Identifieur interne : 002159 ( Main/Exploration ); précédent : 002158; suivant : 002160

Dermatomyositis sine myositis and antisynthetase syndrome.

Auteurs : Ana Climent-Albaladejo [Espagne] ; Encarnacion Saiz-Cuenca ; Juan Rosique-Roman ; Julian Caballero-Rodriguez ; Jose Galvez-Munoz

Source :

RBID : pubmed:11858361

Descripteurs français

English descriptors

Abstract

We describe a 66-year-old woman with cutaneous lesions typical of classic dermatomyositis, clinical evidence of antisynthetase syndrome (arthritis, Raynaud's phenomenon, mechanic's hands and interstitial lung disease with anti-Jo-1 autoantibody) and lack of muscle disease after a full muscle evaluation that included clinical, enzymatic, electromyographic, magnetic resonance imaging and histological studies. The patient did not develop myositis after 9 years of clinical disease. The association of dermatomyositis sine myositis with antisynthetase antibodies suggests that the characteristic skin lesions are closely linked with dermatomyositis on the basis of the similar clinical and serological features of both dermatomyositis sine myositis and classic dermatomyositis.

DOI: 10.1016/s1297-319x(01)00345-1
PubMed: 11858361


Affiliations:


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Le document en format XML

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<term>Chloroquine (therapeutic use)</term>
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<div type="abstract" xml:lang="en">We describe a 66-year-old woman with cutaneous lesions typical of classic dermatomyositis, clinical evidence of antisynthetase syndrome (arthritis, Raynaud's phenomenon, mechanic's hands and interstitial lung disease with anti-Jo-1 autoantibody) and lack of muscle disease after a full muscle evaluation that included clinical, enzymatic, electromyographic, magnetic resonance imaging and histological studies. The patient did not develop myositis after 9 years of clinical disease. The association of dermatomyositis sine myositis with antisynthetase antibodies suggests that the characteristic skin lesions are closely linked with dermatomyositis on the basis of the similar clinical and serological features of both dermatomyositis sine myositis and classic dermatomyositis.</div>
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